infantile myofibromatosis
Introduction
Introduction to infant fibromatosis Infantilemyofibromatosis, also known as congenital generalized fibromatosis, is uncommon and occurs in male infants. basic knowledge The proportion of sickness: 0.01% Susceptible people: good for infants and young children Mode of infection: non-infectious Complications: sarcoidosis
Cause
Causes of infant fibromatosis
(1) Causes of the disease
The cause is still unknown.
(two) pathogenesis
The pathogenesis is still unclear.
Prevention
Infant myofibromatosis prevention
Pay attention to the child's daily life, pay attention to the child's usual diet, and give the child a certain amount of vitamin nutrients.
Complication
Complications of infant myofibromatosis Complications
Generally no special complications.
Symptom
Symptoms of infant fibromatosis common symptoms muscle fibrillation nodules subcutaneous nodules
It is characterized by multiple solid dermis and subcutaneous nodules, which occur at the time of birth or shortly after birth, and occur in the head, neck and trunk. 50% of children develop bone damage. If only skin and bone have fibroids, the prognosis Good, if there is no complication, it is expected that the fibroids will naturally subside when they are 1 to 2 years old.
Fibroids can invade the internal organs including the gastrointestinal tract, breast, lung, liver, pancreas, tongue, serosa, lymph nodes or kidneys. This kind of extensive damage, high mortality, up to 80%, survival for more than 4 months The damage can naturally subside.
Adult single myofibromatosis is a single subcutaneous nodule or mass, common in the head collar, no visceral damage, recurrence is rare.
Examine
Examination of infant myofibromatosis
Histopathology: subcutaneous nodules in the cell area, showing fibroblasts with oval to fusiform nucleus arranged in a bundled or swirling shape. In less cell areas, the interstitial may be mucoid and capillary proliferation.
Diagnosis
Diagnosis and diagnosis of infantile myofibromatosis
According to the clinical manifestations, the characteristics of skin lesions and histopathological features can be diagnosed.
