Buka syndrome
Introduction
Introduction to Buka Syndrome Buka syndrome is caused by inferior vena cava obstruction above the hepatic vein and/or hepatic vein outlet. This disease causes liver stagnation, hepatomegaly, hardening in the late stage, splenomegaly, ascites and portal hypertension. Wait. Common causes are congenital inferior vena cava decidual formation, inferior vena cava thrombosis, primary hepatic vein occlusion, polycythemia vera, oral contraceptives, nocturnal paroxysmal hemoglobinuria, and trauma. The disease is divided into two types: acute and chronic. In the end, hepatic failure and gastrointestinal bleeding can occur due to congestive cirrhosis, and the prognosis is poor. basic knowledge Sickness ratio: 0.0001% Susceptible people: no specific population Mode of infection: non-infectious Complications: abdominal pain, ascites
Cause
Cause of Buka Syndrome
Caused by inferior vena cava obstruction above the hepatic vein and/or hepatic vein outlet.
Prevention
Buka Syndrome Prevention
Pay attention to rest, work and rest, life in an orderly manner, and maintaining an optimistic, positive and upward attitude towards life can be of great help in preventing diseases.
Complication
Buchka syndrome complications Complications abdominal pain ascites
A small number of patients with acute attacks often have other diseases such as renal cancer, primary liver cancer, thrombophlebitis, etc., abdominal pain, vomiting, hepatomegaly, ascites and jaundice can quickly occur in coma and liver failure.
Symptom
Buka syndrome symptoms common symptoms abdominal pain coma liver splenomegaly liver failure edema ascites
Clinical hepatosplenomegaly and tenderness, progressive massive ascites, mild symptoms and other manifestations, the following vena cava obstruction, lower extremity edema, chest and abdominal wall varicose veins, a small number of patients with acute attacks, often suffering from other diseases, such as kidney cancer , primary liver cancer, thrombophlebitis, etc., showing abdominal pain, vomiting, hepatomegaly, ascites and jaundice, can quickly occur convulsions, coma, liver failure and death.
Examine
Inspection of Buka Syndrome
Chronic patients with normal or slightly elevated serum transaminases, prothrombin activity is not low, half of patients with functional renal failure, acute patients with elevated serum transaminase during the onset, thrombin activity decreased.
Imaging examination of the inferior vena cava angiography can be confirmed, Doppler examination can be found above the obstruction of the vein expansion.
Diagnosis
Diagnosis of Buka Syndrome
diagnosis
Imaging examination: Inferior vena cava angiography can be confirmed, Doppler examination can be found above the obstruction of the vein expansion.
Diagnostic identification
1. The acute type is rare, the onset is acute, and the development is rapid. In the short term, it will die from liver failure or gastrointestinal bleeding.
2. Chronic type is more common,
(1) Young adults: The peak age of onset is 25 to 35 years old.
(2) Slow onset: The course of disease is generally 4 to 5 years.
(3) Typical cases often have clinical manifestations of post-hepatic portal hypertension and inferior vena cava obstruction, that is, hepatic, splenomegaly, esophageal varices, thoracic and abdominal varices, depressed edema of both lower extremities, pigmentation of calf skin, heavy The skin is lichen-like or ulcerated. Some patients have symptoms of portal hypertension or the following vena cava obstruction. A few patients have progressive refractory ascites.
(4) B-mode ultrasound examination: It can detect the obstruction of the inferior vena cava and hepatic vein of the hepatic segment, the traffic of hepatic vein and collaterals, and whether there are new organisms in the liver.
(5) vena cava angiography: upper and lower extremity superficial vein cannulation for inferior vena cava end-to-end angiography, can determine the inferior vena cava with or without obstruction, obstruction site, extent, extent, and can also perform vena cava pressure and hepatic venography, cavity The combination of venography and two-dimensional ultrasonography can determine the nature, location, extent and extent of inferior vena cava obstruction, and determine the degree of communication and traffic between the hepatic vein and the inferior vena cava. Vena cava angiography can not only further confirm the diagnosis and can Provide a basis for the selection of surgical treatment options.
(6) Diagnosis is often associated with portal hypertension caused by cirrhosis, cirrhosis ascites, constrictive pericarditis, inferior vena cava syndrome, deep venous thrombosis of the lower extremities and its sequelae, tuberculous peritonitis.
