Birch-Cha Syndrome
Introduction
Introduction to Bai-Cha syndrome Budd-Chiari Syndrome is a syndrome characterized by hepatic dysfunction caused by partial or complete obstruction of the hepatic vein or inferior vena cava. It is also called hepatic vein occlusion syndrome. The intrinsic was reported by Budd and Chiari in 1846 and 1889 respectively. The main clinical features are abdominal pain, hepatosplenomegaly, ascites and lower extremity edema. Intrinsic is relatively rare, can be seen at any age, with 20 to 40 years old. basic knowledge The proportion of illness: 0.035% Susceptible people: no specific population Mode of infection: non-infectious Complications: phlebitis
Cause
The cause of cypress-check syndrome
Causes of intrinsic hepatic veins, inferior vena cava thrombosis, lesions in adjacent organs, and hepatic veins, lesions of the inferior vena cava itself, such as congenital dysplasia, occlusive phlebitis.
Visible thrombosis of the hepatic vein and inferior vena cava, occlusion in the acute phase, inflammatory changes in the chronic hepatic vein, thickening of the vein wall, thrombosis and re-communication of the lumen, hepatosplenomegaly, liver visible under the microscope Central lobular vein dilatation, hepatic sinus congestion, hemorrhage, dilatation, central hepatic atrophy and necrosis, advanced fibrosis in the central lobules, liver tissue regeneration and cirrhosis.
Prevention
Cypress-check syndrome prevention
Prevention of the formation of blood clots is a disease measure to prevent this disease.
Complication
Cypress-diagnosis complications Complications phlebitis
Hepatic vein, inferior vena cava thrombosis, congenital dysplasia of the vein, occlusive phlebitis.
Symptom
Cypress-characteristic syndrome common symptoms varicose abdominal pain hepatosplenomegaly hepatic venous return disorder venous thrombosis jaundice ascites
The intrinsic is mostly chronic, and its clinical manifestations mainly include two aspects:
1. Hepatic venous dysfunction, often with progressive hepatosplenomegaly, esophagus, abdominal varicose veins, ascites and liver pain, abdominal pain, etc., jaundice is rare, in the acute phase of venous thrombosis may have varying degrees of fever and liver District pain, even shock death, late portal hypertension, cirrhosis.
2. Inferior vena cava reflow obstruction, edema of the lower extremities, cyanosis, superficial varices, hyperpigmentation or ulceration, heavy numbness of the lower extremities, and the direction of blood flow of the varicose veins is consistently upward.
Examine
- syndrome check
1. The degree of liver damage is mild, and there may be delayed inoculation of indocyanine green, elevated serum alkaline phosphatase, transaminase, and decreased albumin.
2. B-mode ultrasound and CT examination can show the location, extent, extent and liver morphological changes of hepatic vein and inferior vena cava stenosis and occlusion.
3. Inferior vena cava angiography and selective hepatic venography can accurately determine the location, extent, nature, collateral circulation and external compression of the obstructed lesion.
4. Liver biopsy showed hyperemia and sinusoidal dilatation around the central lobular vein, and cirrhosis in the late stage.
Diagnosis
Diagnosis and identification of Bai-cha syndrome
The main diagnosis is based on hepatosplenomegaly, ascites and characteristic extensive abdominal varices. The intrinsic has three important characteristics:
1. The age is lighter.
2. The characteristics of varicose veins are that the varicose veins are located in the lateral chest, the abdominal wall, and the blood flow direction is also from bottom to top.
3. Although it is like cirrhosis, there is no obvious damage to liver function.
Hepatic vein and inferior vena cava angiography is the main method of diagnosis.
It should be differentiated from cryptogenic cirrhosis, post-hepatitis cirrhosis, portal vein thrombosis and constrictive pericarditis.
