hereditary opalescent teeth
Introduction
Introduction to hereditary opalescent teeth Hereditary dentate malformation (hereditarydentinogenesis imperfecta), also known as hereditary opalescent dentin (hereditary opalescent dentin), is named for its family hereditary and translucent opalescent appearance of teeth. The disease is autosomal dominant, and the permanent teeth can be affected. The coding gene of this disease is located at 4q13. Some patients in this disease are also accompanied by systemic skeletal abnormalities (osteogenesisimperfecta). Germline development is related to abnormalities. basic knowledge The proportion of illness: 0.002% Susceptible people: no specific population Mode of infection: non-infectious Complications: tetracycline teeth
Cause
Hereditary opalescence
The disease is autosomal dominant, and the permanent teeth can be affected. The coding gene of this disease is located at 4q13. Some patients in this disease are also accompanied by osteogenic imperfecta. Therefore, some people think that this disease and Mesoderm dysplasia is related.
Prevention
Hereditary opal prevention
The disease is a hereditary disease and there are currently no effective preventive measures.
Complication
Hereditary opalescent complications Complications tetracycline teeth
Wear can occur, and the dentin is easily worn after exposure, which is manifested by the appearance of a dentin plane after severe abrasion.
Symptom
Hereditary opalescence symptoms Common symptoms Crown is translucent milk color
Under the microscope, the arrangement of dentinal tubules is disordered, the lumen is enlarged, the number of dentinal tubules is reduced in the unit dentin, and the dentinal tubules disappear in some areas. It can be seen that the dentin cells are denatured, the synthetic and secreted matrix proteins are abnormal, and the cells themselves may be Wrapped in the matrix or calcified dentin, the dentin calcification is abnormal. As the tooth is further worn, the repaired dentin is continuously formed in the medullary cavity and the root canal, and at most, the repaired dentin is filled in the entire medullary cavity. .
The enamel thickness and morphology develop normally, but the enamel dentin boundary lacks a zigzag staggered structure, which makes the dentin and enamel have a similar linear joint. The mechanical fitting force is poor, the cementum, periodontal ligament and alveolar bone develop normally. .
The crown is translucent opalescent, which can be light yellow or brownish yellow. The enamel is easily lost. Especially the incisor cutting edge and the molar joint are prone to enamel loss, dentin exposure, dentin. It is easily worn after exposure and appears as a dentin plane after severe abrasion.
The X-ray film showed that the early medullary cavity was larger. After the enamel was removed, the calcified atresia gradually appeared in the medullary cavity and the root canal. The periodontal support tissue was normal, and sometimes the shell tooth was seen, which was characterized by large medullary cavity and dentin. The layer is thin and the root is abnormally short, but there is no root absorption.
Examine
Hereditary opalescent examination
The x-ray film showed that the early medullary cavity was larger. After the enamel was removed, the calcified atresia gradually appeared in the medullary cavity and the root canal. The periodontal support tissue was normal, and sometimes the shell tooth was seen, which was characterized by large medullary cavity and dentin. The layer is thin and the root is abnormally short, but there is no root absorption.
Diagnosis
Diagnosis of hereditary opalescent teeth
diagnosis
Diagnosis can be performed based on clinical manifestations and examinations.
Differential diagnosis
Different from the hereditary tetracycline tooth, excitation fluorescence can be observed by irradiating tetracycline teeth with ultraviolet light, which can be distinguished from hereditary opalescent dentin.
