congenital ulna-radial junction
Introduction
Introduction to congenital ulnar and ulnar joints This is a relatively common congenital deformity of the upper extremities, about 60% of which is bilateral. Since the activity function of children is not yet developed, and the rotation or loss of the disease is limited to the forearm, patients often cannot be detected in time, so neonatal and infant cases are rarely seen. Most of the patients were in the early childhood of 4 to 5 years old. Due to the defects of the movement, the pronation of the hand and the post-spinning activity disappeared, and they were discovered and discovered. basic knowledge The proportion of illness: 0.001% Susceptible people: more common in young children Mode of infection: non-infectious complication:
Cause
Congenital ulnar and ulnar connection
(1) Causes of the disease
The disease refers to the upper and lower ankle joint defects and is connected by bone, which in turn affects the rotation of the forearm. This malformation is autosomal dominant.
(two) pathogenesis
In the process of embryogenesis, the iliac and ulnar bones are homologous to a mesodermal rod-like tissue of the limb bud. If the normal differentiation process is inhibited, it is often manifested that the proximal ends of the two are not completely separated, and the upper ulnar ankle joint is present. connection.
Prevention
Congenital ulnar and ulnar joint prevention
There are no effective preventive measures.
Complication
Congenital ulnar and radial joint complications Complication
There should be no other diseases.
Symptom
Congenital ulnar and ulnar connection symptoms Common symptoms Calcified shoulder movement limitation
1. Clinical manifestations: The patient's fingers, wrists, elbow joints are stretched and flexed normally, but the forearms are fixed at 80°~90° in the pronation. The function of the supination disappears. The children often have external rotation of the shoulder and the elbow flexion is 90°. It is easy to miss the diagnosis by being around to compensate for the rotation.
2. Classification: According to the development of the humeral head, it is divided into 3 types.
(1) Severe type: The upper ankle joint is completely fused into one piece, and the medullary cavity of the two bones is also merged into one, and the humeral head is completely absent.
(2) Moderate type: the humeral head has appeared, but it is stunted, small, pointed and outward; at the neck of the humerus, the ulnar and iliac bones are connected, the range is about 1cm, and the respective bone cortex of the ulna and the tibia can be seen. Exist, but tightly connected.
(3) Mild type: The humeral head is fully differentiated and developed. There is an interosseous ligament calcification between the ruler and the tibia to become a bone bridge, which limits the rotation of the humerus.
3. X-ray film can be clearly diagnosed; however, the bone is not completely calcified before the child is 2 to 4 years old, and the diagnosis is not easy.
Examine
Congenital ulnar and tibial connection
X-ray examination can confirm the diagnosis.
Diagnosis
Diagnosis and diagnosis of congenital ulnar and radial joints
The disease needs to be distinguished from the traumatic ulnar bridge: the latter has a history of trauma, the ulna, the tibia itself is well developed, not shortened, the humeral head is well developed, and the bone connection is mostly in the interosseous membrane area.
